Congenital Malformations Registry - 1996 Report

Appendix 4

BPA Codes

Many birth defects registries use a coding system modified from the British Pediatric Association (BPA). This coding system provides more specificity than the ICD-9 system. The Centers for Disease Control and Prevention Metropolitan Atlanta Congenital Defects Program (MACDP) has developed codes that group conditions. The table below shows the MACDP codes and the corresponding BPA and ICD-9 codes. The ICD-9 code may include conditions others than those specified by the BPA code. For example, ICD-9 code 756.7 includes both gastroschisis and omphalocele, but the BPA code allows these conditions to be distinguished.

MACDP CodeConditionICD-9BPA 5-Digit Code
CENTRAL NERVOUS SYSTEM
A01Anencephaly740.0, 740.1, 740.2740.00, 740.02, 740.03, 740.10, 740.20, 740.21, 740.29
A02Spina Bifida with Hydrocephaly741.0741.00, 741.01, 741.02, 741.03, 741.04, 741.05, 741.06, 741.07, 741.08, 741.09
A03Spina Bifida without Hydrocephaly741.9741.90, 741.91, 741.92, 741.93, 741.94, 741.98, 741.99, 742.00, 742.08, 742.09
A13Encephalocele742.0742.00, 742.08, 742.09
A15Hydrocephaly742.3742.30, 742.31, 742.38, 742.39
A16Microcephalus742.1742.10
EYE / EAR
B01Anophthalmia, Microphthalmia743.0, 743.1743.00, 743.10
B03Glaucoma743.2743.20, 743.21, 743.22
B04Cataract 743.32
B54

Ear anomaly with hearing loss744.0744.00, 744.01, 744.02, 744.03, 744.09, 744.21
CARDIAC
D01Truncus arteriosus745.0745.00, 745.01
D02Transposition of great vessels745.1745.10, 745.11, 745.12, 745.18, 745.19
D03Tetralogy of Fallot745.2 745.20, 745.21, 746.84
D04Single ventricle745.3745.30
D05VSD745.4745.40, 745.41, 745.48, 745.49
D52Hypoplastic left heart746.7746.70
D53Total anomalous pulmonary venous return747.41747.42
RESPIRATORY
E01Choanal atresia748.0748.00
E06Agenesis of lung748.5748.50, 748.51
CLEFTS
F01Cleft palate749.0749.00, 749.01, 749.02, 749.03, 749.04, 749.05, 749.06, 749.07, 749.09
F02Cleft lip with or without cleft palate749.0, 749.2,

750.5

749.10, 749.11, 749.12, 749.19, 749.20, 749.21, 749.22, 749.29, 749.51
GASTRO-INTESTINAL
F14Stenosis or atresia of duodenum751.1751.10
F15Other stenosis or atresia of small intestine751.1751.11, 751.12, 751.19
F16Stenosis or atresia of rectum or anus751.2751.21, 751.22, 751.23, 751.24
F17Hirschsprung's Disease751.3751.30, 751.31, 751.32, 751.33
F18Malrotation of intestine751.4751.40, 751.41, 751.42, 751.49
F21Biliary atresia751.61751.65
GENITO-URINARY
H01Renal agenesis753.0753.00, 753.01
H06Obstruction of kidney or ureter753.3753.20, 753.21, 753.22, 753.29, 753.40, 753.42
H09Bladder or urethra obstruction753.6753.60, 753.61, 753.62, 753.63
MUSCULOSKELETAL
J02Curvature of spine (scoliosis or lordosis)754.2754.20, 754.21, 754.22
J03Dislocation of hip754.3754.30
J11Arthrogryposis multiplex congenita754.89755.80
K01Reduction deformity - upper limb755.2755.20, 755.21, 755.22, 755.23, 755.24, 755.25, 755.26, 755.27, 755.28, 755.29
K02Reduction deformity - lower limb 755.30, 755.31, 755.32, 755.33, 755.34, 755.35, 755.36, 755.37, 755.38, 755.39
K05Amniotic bands658.8658.80
N01Diaphragmatic hernia756.6756.61
N02Omphalocele756.7756.70
N04Gastroschisis756.7756.71
SYNDROMES
R01Down Syndrome758.0758.00, 758.01, 758.02, 758.03, 758.04, 758.09
R02Patau Syndrome (Trisomy 13)758.1758.10, 758.11, 758.12, 758.13, 758.19
R03Edwards Syndrome (Trisomy 18)758.2758.20, 758.21, 758.23, 758.29
S02Fetal Alcohol Syndrome760.71760.71
W03Conjoined twins759.4759.40, 759.41, 759.42, 759.43, 759.44, 759.48, 759.49