Congenital Malformations Registry - Summary Report

Appendix 4

BPA Codes

Many birth defects registries use a coding system modified from the British Pediatric Association (BPA). This coding system provides more specificity than the ICD-9 system. The Centers for Disease Control and Prevention Metropolitan Atlanta Congenital Defects Program (MACDP) has developed codes that group conditions. The table below shows the MACDP codes and the corresponding BPA and ICD-9 codes. The ICD-9 code may include conditions others than those specified by the BPA code. For example, ICD-9 code 756.7 includes both gastroschisis and omphalocele, but the BPA code allows these conditions to be distinguished.

MACDP Code Condition ICD-9 BPA 5-Digit Code
A01 Anencephaly 740.0, 740.1, 740.2 740.00, 740.02, 740.03, 740.10, 740.20, 740.21, 740.29
A02 Spina Bifida with Hydrocephaly 741.0 741.00, 741.01, 741.02, 741.03, 741.04, 741.05, 741.06, 741.07, 741.08, 741.09
A03 Spina Bifida without Hydrocephaly 741.9 741.90, 741.91, 741.92, 741.93, 741.94, 741.98, 741.99, 742.00, 742.08, 742.09
A13 Encephalocele 742.0 742.00, 742.08, 742.09
A15 Hydrocephaly 742.3 742.30, 742.31, 742.38, 742.39
A16 Microcephalus 742.1 742.10
B01 Anophthalmia, Microphthalmia 743.0, 743.1 743.00, 743.10
B03 Glaucoma 743.2 743.20, 743.21, 743.22
B04 Cataract   743.32
B54 Ear anomaly with hearing loss 744.0 744.00, 744.01, 744.02, 744.03, 744.09, 744.21
D01 Truncus arteriosus 745.0 745.00, 745.01
D02 Transposition of great vessels 745.1 745.10, 745.11, 745.12, 745.18, 745.19
D03 Tetralogy of Fallot 745.2 745.20, 745.21, 746.84
D04 Single ventricle 745.3 745.30
D05 VSD 745.4 745.40, 745.41, 745.48, 745.49
D52 Hypoplastic left heart 746.7 746.70
D53 Total anomalous pulmonary venous return 747.41 747.42
E01 Choanal atresia 748.0 748.00
E06 Agenesis of lung 748.5 748.50, 748.51
F01 Cleft palate 749.0 749.00, 749.01, 749.02, 749.03, 749.04, 749.05, 749.06, 749.07, 749.09
F02 Cleft lip with or without cleft palate 749.0, 749.2, 750.5 749.10, 749.11, 749.12, 749.19, 749.20, 749.21, 749.22, 749.29, 749.51
F14 Stenosis or atresia of duodenum 751.1 751.10
F15 Other stenosis or atresia of small intestine 751.1 751.11, 751.12, 751.19
F16 Stenosis or atresia of rectum or anus 751.2 751.21, 751.22, 751.23, 751.24
F17 Hirschsprung  s Disease 751.3 751.30, 751.31, 751.32, 751.33
F18 Malrotation of intestine 751.4 751.40, 751.41, 751.42, 751.49
F21 Biliary atresia 751.61 751.65
H01 Renal agenesis 753.0 753.00, 753.01
H06 Obstruction of kidney or ureter 753.3 753.20, 753.21, 753.22, 753.29, 753.40, 753.42
H09 Bladder or urethra obstruction 753.6 753.60, 753.61, 753.62, 753.63
J02 Curvature of spine (scoliosis or lordosis) 754.2 754.20, 754.21, 754.22
J03 Dislocation of hip 754.3 754.30
J11 Arthrogryposis multiplex congenita 754.89 755.80
K01 Reduction deformity - upper limb 755.2 755.20, 755.21, 755.22, 755.23, 755.24, 755.25, 755.26, 755.27, 755.28, 755.29
K02 Reduction deformity - lower limb   755.30, 755.31, 755.32, 755.33, 755.34, 755.35, 755.36, 755.37, 755.38, 755.39
K05 Amniotic bands 658.8 658.80
N01 Diaphragmatic hernia 756.6 756.61
N02 Omphalocele 756.7 756.70
N04 Gastroschisis 756.7 756.71
R01 Down Syndrome 758.0 758.00, 758.01, 758.02, 758.03, 758.04, 758.09
R02 Patau Syndrome (Trisomy 13) 758.1 758.10, 758.11, 758.12, 758.13, 758.19
R03 Edwards Syndrome (Trisomy 18) 758.2 758.20, 758.21, 758.23, 758.29
S02 Fetal Alcohol Syndrome 760.71 760.71
W03 Conjoined twins 759.4 759.40, 759.41, 759.42, 759.43, 759.44, 759.48, 759.49